Pulmonary lymphangiectasia a rare cause of chylothorax: A case report

Background: Pulmonary lymphangiectasia (PL) is a rare disease characterized by dilation of the pulmonary lymphatic vessels. PL should be considered in differential diagnosis infants with pleural effusion, especially presence chylothorax. Case Presentation: A 3-week-old neonate presented tachypnea, cough, and reluctance to feed. Work-up found bilateral chylous effusion. The patient was initially managed conservatively tube thoracostomies octreotide, however output from chest tubes did not subside. left thoracotomy performed wedge biopsy apical segment inferior lung lobe multiple titanium clips were used control thoracic duct. Postoperatively continued have high output, despite placement clips. Histology confirmed congenital lymphangiectasia. Conclusion: cause treatment often challenging as index case.